We describe three cases of a fibroinflammatory pseudotumor tumefactive fibroinflammatory lesion of the middle and inner ear. Pdf enfermedad inflamatoria orbitaria asociada a igg4. Orbital pseudotumor disguised as orbital cellulitis and. Macroscopic appearance hepatic ipt is often seen a. First described by birchhirschfield in 1905, idiopathic orbital inflammatory syndrome, also known as orbital pseudotumor, is a nonspecific, nonneoplastic inflammatory process of the orbit. However, inflammatory pseudotumor has been reported to occur in a variety of anatomical sites, including the gastrointestinal tract and the central nervous system. Volume 27, issue 6, novemberdecember 2016, pages 291295. Inflammatory pseudotumor was first observed in the lung and described by brunn in 1939 and was so named by umiker et al in 1954 because of its propensity to clinically and radiologically mimic a malignant process, 1. Among 27 cases in which surgery was performed, thoracotomy was performed in 23 cases. Vilas boas rms, madeira ia, lopes aa, paiva eb, rodrigues as. Orbital pseudotumor op or idiopathic orbital inflammatory disease was first described in 1903 by gleason and by busse and hochheim 4. Microsofts free reader application, or a booksized computer this is used solely as a. Inflammatory pseudotumor is a quasineoplastic lesion that most commonly involves the lung and the orbit, but it has been reported to occur in nearly every site in the body. Pulmonary inflammatory pseudotumor needs to be distinguished from sclerosing hemangioma, pseudolymphoma and malignant sarcoma 12.
Adenomyosis is formed by the invagination of the basalis layer along the intramyometrial. We preoperatively could not rule out the possibility of a malignant neoplasm, due to the fact that the tumor had grown in size after a 2year observation. It is the most common painful orbital mass in the adult population, and is associated with proptosis, cranial nerve palsy tolosahunt syndrome, uveitis, and retinal detachment. Since that time, inflammatory pseudotumor has been described in the literature by many different names, table 1, a fact that suggests the complexity and. Alguns estudos demonstraram processo inflamatorio inespecifico do seio cavernoso, envolvendo a arteria carotida por contiguidade. Inflammatory pseudotumor of the posterior mediastinum. Pseudotumor orbitario refractario tratado con rituximab en. Pdf sclerosing orbital pseudotumor is a rare subtype of idiopathic orbital inflammatory pseudotumor. Pseudotumor orbitae is a rare and uncommon disease including idiopathic benign inflammatory alterations with sudden onset of exophthalmus, reduced eye motility, swelling of soft tissue and heavy pain together with a tumor formation, which may even simulate a neoplastic process. Orbital pseudotumor is an uncommon disorder that both radiologically and clinically mimics a malignant process or other inflammatory disease, such as graves ophthalmopathy. Less commonly there is inflammatory change involving the uvea, sclera, lacrimal gland, and retrobulbar soft tissue. Hepatic inflammatory pseudotumor radiology reference.
Periaortitis definition of periaortitis by medical dictionary. O pseudotumor inflamatorio, ou tumor miofibroblastico inflamatorio tmi, e uma afeccao rara e com aspectos ainda pouco compreendidos, representando um dilema pela semelhanca com processos. Celulitis orbitaria pseudotumor inflamatorio leucemia neuroblastoma metastsico. Pseudotumor inflamatorio orbitario forma difusa y presentacion aguda. Local invasion and primary involvement of the mediastinum and hilar structures were unusual manifestations. Surgery and steroid treatment jianfeng zhu1, weijiao zhan1, lihua wang2 and yanhong wang3 1department of ophthalmology, linyi municipal hospital, linyi 276003, 2department of ophthalmology, provincial hospital.
Usually presented as a large liver mass, may cause. Education exhibit continuing medical educationfree access. Idiopathic orbital inflammatory syndrome, also known as orbital pseudotumor, was. The computed tomographic pattern showed destruction of inner ear. Pulmonary inflammatory pseudotumor was typically a solitary, peripheral, sharply circumscribed mass with an anatomic bias for the lower lobes. A case of a woman 43 years old with palpebral inflamation in her right. The ocular manifestations of orbital pseudotumor may include periorbital. Edematous tissue with excessive production of ground substance, chronic inflammatory cells, vascular proliferation and hyperplastic connective tissue may have periphlebitis with tissue eosinophilia. Pseudotumor inflamatorio hepatico, tumor miofibroblastico, recurrencia, reseccion hepatica. To provide an overview of the spectrum of diseases known as idiopathic orbital inflammatory syndrome also known as orbital pseudotumor, with emphasis on.
The diagnosis was orbital cellulitis and sinusitis. Clinically, orbital pseudotumor has been categorized as myositis, dacryoadenitis, anterior, apical and diffuse process. Inflammatory pseudotumor is a rare tumor of unknown origin that predominantly affects the lung and the orbit. Eight days after the steroid treatment significant radiological and clinical improvement was observed. The authors present the case of an 81yearold man with hypertension and alcohol consumption 6080 gday who was admitted to the emergency department with abdominal pain in the upper right quadrant, with 1 month of evolution, diarrhea 56 liquid stools per day, and slimming of. Inflammatory pseudotumor ipt is a rare benign lesion histologically characterized by the presence of a heterogeneous population of inflammatory cells, particularly plasma cells, macrophages and fibroblasts, as well as areas of fibrosis and necrosis.
Enfermedad inflamatoria orbitaria idiopatica request pdf. A case of a 45yearold japanese man with a splenic inflammatory pseudotumor is described. Inflammatory pseudotumor ipt of the liver is a rare disease characterized by chronic infiltration of inflammatory cells. Fibroinflammatory pseudotumor of the ear a locally. Histological findings were consistent with an inflammatory pseudotumor, and steroid treatment allowed the disappearance of all the lesions. Dd include orbital cellulitis, wegener granulomatosis and lymphoma. Combinations of fibroblasts and myofibroblasts in background of plasma cells and other inflammatory cells. However, after performing a splenectomy, a histological examination of the mass. Idiopathic orbital inflammatory ioi disease, refers to a marginated masslike enhancing soft tissue involving any area of the orbit.
Infiltrado inflamatorio cronico y fibrosis esclerosante. Inflammatory pseudotumors of the pituitary are very rare. Surgery is the treatment of choice in pulmonary inflammatory pseudotumor to distinguish between malignant tumors 18, 19, 22, 23. The patients presented with total deafness in the affected ear and no response to caloric stimulation. Semiologia e imagenes en patologia orbitaria sarcoma. Orbital pseudotumor is an idiopathic inflammatory condition that usually involves the extraocular muscles although, in some cases there is inflammatory change involving the uvea, sclera, lacrimal gland and retrobulbar soft tissues. Inflammatory pseudotumour of the infratemporal fossa. A read is counted each time someone views a publication summary such as the title, abstract, and list of authors, clicks on a figure, or views or downloads the fulltext. Orbitopatia inflamatoria trastornos oftalmicos manual msd.
A 58yearold man with a past medical history of chronic sinus disease and hypothyroidism presented with left periorbital pain and erythema that worsened despite outpatient treatment with topical antibiotics. An ebook reader can be a software application for use on a computer such as microsofts free reader application, or a booksized computer. Hepatic inflammatory pseudotumors ipt are rare benign hepatic lesions. This benign lesion is rarely reported in the world literature. Epidemiology most common in young adults with males affected more than females 7. O pseudotumor orbital idiopatico e uma inflamacao orbitaria nao maligna sem. Idiopathic inflammatory pseudotumor of the carotid sheath. An ebook reader can be a software application for use on a computer such as microsofts free reader application, or a booksized computer this is used solely as a reading device such as nuvomedias rocket ebook. Idiopathic orbital inflammation radiology reference.
Yousem1 abstract we present a biopsy proven case of 47 yearsold man with a carotid pseudotumor, clinically pre. An outpatient ct scan showed pansinusitis and orbital stranding. The patient was suspected to have an inflammatory process and steroids were prescribed. According to the who classification, three lesional patterns can be observed inflammatory. Pseudotumor inflamatorio del seno frontal asociado a. This case appears unique with regard to the extension of the lesions and the dramatic response to medical treatment.
Extensive inflammatory pseudotumor of the pituitary the. Inflammatory pseudotumor most often occurs in the lung, liver, and orbit but it has been reported to occur in nearly every organ in the body 5,6. Idiopathic orbital inflammation ioi, also known as orbital pseudotumor and nonspecific orbital inflammation, is an idiopathic inflammatory condition that most commonly involves the extraocular muscles. Orbital melanocytic sarcoma as manifestation of leukemia.
1607 1291 1602 361 763 1166 370 327 352 1136 900 818 1047 640 953 68 1043 1359 435 1485 574 115 1052 1049 494 768 1195 705 1194 1601 1098 832 451 1419 167 724 172 458 1357 361 711